Sandeep Kumar Kar, Tanmoy Ganguly and Swarnali Dasgupta
Malignant peripheral nerve sheath tumour (MPNST) is a rare and very aggressive tumour of nerve cell origin associated with poor prognosis. Incidence of MPNST is 1 per 1, 00,000 populations and it constitutes between 3%-10% of all soft tissue sarcomas1-4. MPNST have been found to be associated with neurofibromatosis type 1 (associated with mutation in NF-1 gene) in 2%-29% cases . Male and female are almost equally (53:47) involve. These tumours often create diagnostic dilemmas because of non-specific clinical diagnostic criteria, histopathological resemblance with other spindle cell sarcomas like monophasic synovial sarcoma, leiomyosarcoma and fibrosarcoma.
इस लेख का हिस्सा
English 
Spanish 
Chinese 
Russian 
German 
French 
Japanese 
Portuguese 
Telugu 